Secondary Budd-Chiari Syndrome due to Sarcomatous Renal Cell Carcinoma: Case Report

Sarcomatoid renal carcinoma represents 8% of all renal tumors, is caused by any of the renal carcinoma subtypes and is characterized by high cellularity, cellular atypia, and epithelial and mesenchymal components. Sarcomatoid renal cell carcinomas usually have a poor response to systemic treatment, and most patients survive on average 4 to 9 months after diagnosis. Budd Chari syndrome is a rare disease caused by obstruction of the hepatic venous system. If the cause is an endoluminal lesion, it is considered a primary syndrome, while if the cause is external to the venous system, it is considered a secondary syndrome. We present the clinical case of a patient with a sarcomatoid carcinoma that caused a secondary Budd Chiari syndrome with a rapid and aggressive evolution that culminated in multiple organ failure and the death of the patient.

Keywords: Budd-Chiari Syndrome

Abbreviations: BCS: Budd Chiari syndrome; DVT: Deep vein thrombosis; SRCC: Sarcomatous renal cell carcinoma; SAAG: Serum ascites albumin gradient